Authors:

Frankie OG Fraulin*

Alberta Children�s Hospital, Sections of Plastic Surgery and Pediatric Surgery, Department of Surgery, University of Calgary Shaganappi Trail Northwest, Calgary, Alberta

Abstract:

In the current study, a 15-year-old girl with genetically proven de novo neurofibromatosis is described. She has two arteriovenous malformations (AVMs) on her left labia majora and left thigh. Using emboli-zation methods, it was particularly challenging to treat the patient�s labia majora AVM. She suffered from pulmonary edoema, venous thromboemboli, severe localised necrosis, and a compromised anal sphincter, among other problems. Her suprapubic and perineal regions needed to be surgically debrided and rebuilt. Later, the left thigh AVM was successfully treated with a combination of surgical excision and embolization, with no sequelae. After six years, she is still doing well. The current study is the only extracranial arteriovenous malformations and neurofibromatosis case that has been documented in the literature, to the authors� knowledge.
Keywords:
Labia majora, multiple, neurofibromatosis type 2, complications, embolization, and arteriovenous malformation

Citation:

Frankie OG Fraulin. Treatment of a Rare Case of Multiple Arteriovenous Malformations in the Context of Neurofibromatosis. World Journal of Clinical Surgery 2022.